M E D I C U S - Shoqata e Mjekëve Shqiptarë të Maqedonisë-Hipokrati

M E D I C U S - Shoqata e Mjekëve Shqiptarë të Maqedonisë-Hipokrati M E D I C U S - Shoqata e Mjekëve Shqiptarë të Maqedonisë-Hipokrati

14.01.2013 Views

Figure 1 a- Skeletal abnormalities (long, thin extremities). Figure 1 b- Arachnodactly in the same patient. Fundus evaluation showed bilateral spontaneous posterior lens dislocation associated with total rhegmatogenous retinal detachment in the right eye (Figure 2 a-b). Ultrasonography of the right eye revealed spikes consistent with a total rhegmatogenous retinal detachement and a posterior dislocated lens (Figure 2 c). Figure 2 Here ... (from left to right) Figure 2 a- The lack of the lens. Figure 2 b- Fundoscopic view of total rhegmatogenous retinal detachment. Figure 2 c- Ultrasound examination of the right eye – Retinal detachment and presumed lens material in the vitreous cavity. The patient underwent successful retinal detachment surgery (PPV + SOI) in the right eye and had visual acuity of 4/20, (+6.5 D/+1.00 X 10°) at 6 months follow up (Figure 3 a-b). She had also antiglaucomatous therapy for the left eye, but with poor results (presence of vitreous in the anterior chamber). She was referred to a cardiologist and she had a complete check up and future following up plan.

Figure 3 Here ... Figure 3 a- Right eye fundoscopic view 6 months after surgery. Figure 3 b- Ultrasound examination of the same eye. CASE PRESENTATION II Her little sister (24 yrs old) came to our clinic after we called her. She had had no ophthalmic examinations in the past (!!!). She complained for blurred vision in both eyes. On systemic examination she also had skeletal abnormalities (long, thin extremities), arachnodactly and high-arched palate; findings consistent with diagnosis of Marfan's Syndrome. Ocular examination revealed in the right eye a visual acuity of 6/20 (sph.+6.5) and 6/20 (sph. + 8.5 D) in the left eye. Intraocular pressure was 17.3 mm Hg both eyes. Fundus evaluation showed bilateral spontaneous posterior lens dislocation associated with retinal thinning and degeneration but no tears (Figure 4-5). Figure 4 Here ... Figure 4 a- Right eye, the lack of the lens. Figure 4 b- Fundoscopic view of the same eye.

Figure 1 a- Skeletal abnormalities (long, thin extremities).<br />

Figure 1 b- Arachnodactly in the same patient.<br />

Fundus evaluation showed bilateral spontaneous posterior lens dislocation<br />

associated with total rhegmatogenous retinal detachment in the right eye (Figure 2 a-b).<br />

Ultrasonography of the right eye revealed spikes consistent with a total<br />

rhegmatogenous retinal detachement and a posterior dislocated lens (Figure 2 c).<br />

Figure 2 Here ... (from left to right)<br />

Figure 2 a- The lack of the lens.<br />

Figure 2 b- Fundoscopic view of total rhegmatogenous retinal detachment.<br />

Figure 2 c- Ultrasound examination of the right eye – Retinal detachment and presumed lens<br />

material in the vitreous cavity.<br />

The patient underwent successful retinal detachment surgery (PPV + SOI) in the<br />

right eye and had visual acuity of 4/20, (+6.5 D/+1.00 X 10°) at 6 months follow up<br />

(Figure 3 a-b). She had also antiglaucomatous therapy for the left eye, but with poor<br />

results (presence of vitreous in the anterior chamber). She was referred to a cardiologist<br />

and she had a complete check up and future following up plan.

Hooray! Your file is uploaded and ready to be published.

Saved successfully!

Ooh no, something went wrong!