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medulla spinalis

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Ön Boynuz Sendromları İzole olarak ön boynuz hücrelerinde yıkım vardır.Kraniyel motor nükleuslar da etkilenebilir.Diffüz spinal musküler atrofiler o İnfantil progresif SMA (Werdnig-Hoffman, Tip I SMA)o İntermediate SMA (Tip II SMA)o Juvenil progresif SMA (Kugelberg-Welander hastalığı)o MNHda progresif SMABelirDler: Güçsüzlük Atrofi Fasikülasyon DTR azalır, hipotoni

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