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Prader-Willi syndrom nov 10[1].pdf

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Könshormon PWS män<br />

JCEM 2009, HJ Hirsch et al<br />

• Dåligt utvecklade könsorgan<br />

• Försenat och inkomplett pubertet<br />

• De flesta dåligt fungerande testiklar, få hypofyshypothalamus<br />

svikt<br />

• Fertila män ej beskrivna

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