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6 mesi di terapia enzimatica (Cerezyme):<br />
P: Kg 14,5 (+ Kg 1); H: cm 101 (+ cm 6,5)<br />
• Epatosplenomegalia clinicamente non più rilevabile<br />
• Es. emocromocitometrico:<br />
GR: 4.340.000; Hb 12.2 gr/dL (+ 1,9 gr/dL); Hct: 34.4 (+<br />
3,4%); PLT: 249000/mmc<br />
• chitotriosidasi: 2978 nmol/h/ml (vn