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GLUTARICO ACIDEMIA TIPO I<br />
LYS TRP<br />
ac.3-OH-antranilico<br />
Ac.2-aminoadipico OH-LYS<br />
ac.2-oxoadipico<br />
glutaril-CoA acido glutarico<br />
glutarilcarnitine glutaconil-CoA acido glutaconico<br />
crotonil-CoA acido 3-OH-glutarico<br />
acetoacetil-CoA