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Giacomo Biasucci pdf - Sipps

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GLUTARICO ACIDEMIA TIPO I<br />

LYS TRP<br />

ac.3-OH-antranilico<br />

Ac.2-aminoadipico OH-LYS<br />

ac.2-oxoadipico<br />

glutaril-CoA acido glutarico<br />

glutarilcarnitine glutaconil-CoA acido glutaconico<br />

crotonil-CoA acido 3-OH-glutarico<br />

acetoacetil-CoA

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