Abstracts Posters SICOT-SOF meeting Gothenburg 2010 _2_

Poster
Topic: Tumours
Abstract number: 25230
POLYOSTOTIC FIBROUS DYSPLASIA WITH ULNAR NERVE DYSFUNCTION
Luis COLL MESA, Nieves HERNANDEZ DE LEON, Manuel GONZALEZ GAITANO,
Julio VEGA SANGINES, Pedro Javier PEREZ LORENSU, Maria PORRAS
SANCHEZ
Hospital Universitario de Canarias, Puerto de la Cruz ( Tenerife ) (SPAIN)
Fibrous dysplasia is a benign medullary fibro-osseous disease in which normal
marrow and cancellous bone are replaced and weakened by immature woven bone
and a dense fibroticstroma containing a disorganized matrix of bony trabecular
spicules.This skeletal tumor may involve one bone (monostotic) or multiple bones
(polyostotic) and occurs throughout the skeleton with a predilection for the long
bones, ribs, and craniofacial bones.The lesion is often asymptomatic but pain,
swelling, bony expansion in superficial bone and fractures may be part of the clinical
spectrum. Neurological symptoms are very uncommon.We present a case of a 55
year-old woman who was referred to us presenting pain in her left elbow and
symptoms of ulnar nerve dysfunction. The radiological study showed cortical and
cancellous bone defects involving left distal humerus, proximal ulna and radius with
margins well defined, bone sclerosis areas and thinned and expanded cortex near
epitrochlear canal. The diagnosis of Polyostotic Fibrous Dysplasia was confirmed by
biopsy.The treatment of choice was resection of exostosis and neurolysis achieving a
complete recovery of the ulnar nerve function.In conclusion, clinical symptoms in
conjunction with radiological findings and biopsy are useful tools in the diagnostic
and operative planning of Fibrous Dysplasia and surgery can be indicated for
correction of deformity, prevention of pathologic fracture, and/or eradication of
symptomatic lesions.
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