Boston - American Association for Thoracic Surgery

AMERICAN ASSOCIATION FOR THORACIC SURGERYRESULTS: Follow-up was 94% complete. 30-day and late mortality after definitivesurgery in all 236 patients was 6% (n = 13) and 6% (n = 14), respectively. Overallsurvival was 89% at 3 years following definitive repair. 203 patients (85%) haddefinitive repair at a median age of 2.0 years. There was no significant difference insurvival following complete repair between patients from any of the three morphologicalpulmonary artery groups (P = 0.18). 132 (56%) patients had complete repairwith VSD closure, as a single or staged procedure in 111 and 21 patients, respectively.Focalisation of MAPCAs with proven long-term patency with the RV wasassociated with a survival benefit compared to 14 patients in whom unifocalisationwas not possible and had only systemic shunts. In the follow-up period, 190patients required 196 catheter and 60 surgical re-interventions.CONCLUSION: Using a strategy of unifocalisation, intrapericardial pulmonaryartery reconstruction and RV-PA conduit, excellent long-term survival can beachieved in this group of patients even in the absence of native intrapericardialpulmonary arteries.TUESDAYAfternoon193