Index 379 gastrostomy tube, 84-85, 91, 346 genes and gene products, 39-40; FANCA, 39-40, 44-46, 277-278, 281; FANCB, 39-40, 44, 276; FANCC, 39-40, 44-46, 52, 136, 277-278, 281, 285; FANCD1/BRCA2, 39, 40, 44-46, 50, 52, 200, 202, 210, 225, 229-230, 233, 276 278, 280-282, 284; FANCD2, 39-40, 43-44, 46; FANCE, 39-40, 278; FANCF, 39-40, 278; FANCG (XRCC9), 39-40, 45-46, 277-278, 281; FANCI (KIAA1794), 39-40, 46; FANCJ (BACH1, BRIP1), 39-40, 44, 276, 282, 284; FANCL (PHF9/POG), 39-40, 44; FANCM (hef), 39-40, 44; FANCN/PALB2, 39-40, 44, 46, 50, 52, 276, 281-282, 284-285 gene therapy, 236-238; stem cell gene therapy, 240-242; stem cell therapy, 238-240 genetic counseling, 275-290; genetic testing, 277-279, see also mutation analysis; complementation groups; mode of inheritance, 275-277; reproductive issues, 285 genital warts, 123 genotype-phenotype correlations, see complementation groups giardia antigen, 80, 347 ginkgo, 204 glomerular filtration rate (GFR), 186, 210, 347 glucocorticoids, 147, 158, 227 glucose abnormalities, abnormal lipid profile with glucose intolerance, 150; abnormal metabolism of, 134, 145-147; in adults, 156-157, 160, 268; during or post-HSCT, 158, 182, 228, 232; glucose intolerance assessment and monitoring, 87, 138, 140, 146-147, 359; incidence of in FA, 139; medications known to alter glucose metabolism, 86, 147; treatment of, 147-148 gonads, gonadal function, abnormalities, 121, 138-139, 154, 347, 351; adults, hypogonadism in, 151, 156; effect of iron overload on, 68; Cytoxan, effect on, 158; fertility, hypogonadism effect on, 128; HSCT effect on, 159, 191, 227; puberty, gonadal deficiency effect on, 151-152; screening for, 43, 138-139 graft-versus-host disease, see transplants, graft-versus-host disease grieving process, 291, 304, 307; cognitive changes due to, 309; and the physician’s role, 307-316; stages of, 308-310; physical changes due to, 309; self-destructive behavior from, 309 growth, 82-83, 140, 152, 159-160, 200-201; androgen therapy effect on, 58, 157-158; bone therapy, 155; cortisol sufficiency, 138, 150, 340; hemoglobin level necessary for, 66; hormone deficiency, 134-135, 142-145, 227; hormone deficiency
380 <strong>Fanconi</strong> <strong>Anemia</strong>: Guidelines for Diagnosis and Management post-transplant, 227-228; hormone, screening for, 138; incidence of low growth hormone, 139, 157; iron overload, effect on, 68; monitoring post-transplant, 224, 227, 232; pubertal delay, effect on, 122, 152, 153; radiation, effect on, 191; rate and bone maturation, 137-138; thyroid, effect on, 140-142, see also thyroid; treatment for, 144-145, 202, 228 growth plate, see epiphyseal closure gynecologic and fertility issues in females, 121-133; abnormal uterine bleeding, 123-124; cancer, see cancer for specific type; cervical cytology testing, 122, 125; dysplasia, 123, 125, 131; fertility, see fertility; genital tract malformations, 121, 131, 154; gynecologic cancer, see cancer, types of, gynecological; exam, 122-123; gynecological issues related to HSCT, 127-128; human papillomavirus, see cancer, types of, HPVassociated; vaccination/immunizations; mammograms, see mammography; menopause, see menopause; menses, 35, 121- 123; osteoporosis, see osteopenia/osteoporosis; pregnancy, see pregnancy; puberty, see puberty; uterine polyps, 124 gynecomastia, 283, 348 H2-antagonists, 50, 81, 348 hair, facial, pubic, scalp, 58, 212-214, 218 hand and arm differences, 97-120; emotional issues related to, 117- 118; testing to rule out FA, 98 head and neck squamous cell carcinoma (HNSCC), 250-263, 267; age of presentation of, 252, 255; characteristics of in FA, 252; chemotherapy treatment of, 261; cytotoxic treatment, atypical response to, 252; diagnosis and evaluation, 255-257; dysplasia, 256-257; frequency of in FA, 253; human papillomavirus, see vaccination/immunizations; in non-transplanted patients, 36; incidence of, 250-252; non-FA SCC patients without normal risk factors, testing for FA in, 251-252; prevention of, 190, 217, 253-255; radiation treatment of, 259-261; risk for developing, 37, 144, 190, 251, 261; surgical treatment of, 258-259; surveillance for, 204, 217, 255-257, 260-261, 267; symptoms, presenting symptoms, 253; tobacco and alcohol use risks, see smoking; alcohol; T-stage, 259 hearing and ear abnormalities, 165-177; hearing and ear screening for family members, 175 hearing loss, amplification systems, 171-174; diagnostic tests, 167- 168, 170, 175-176, 230-231, 335, 337; early identification and intervention for 170-171; iron chelator, possible effect of, 175; surgical management of, 172-174; types of, 35, 166-174, 261;
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