guidebook. - Fanconi Anemia Research Fund

116
Fanconi Anemia: Guidelines for Diagnosis and Management
Figure 13: Four-year-old child with recurrent deformity of the left
wrist treated with distraction histiogenesis using an Ilizarov device
to stretch the taut soft tissue structures.
the treatment regimen, and preoperative education is
critical (Figure 13).
This sophisticated form of treatment introduces additional
complications that require discussion prior to
surgery, such as pin tract infection, fracture of the
regenerated bone, and digital stiffness. On occasion,
adolescents with shortened forearms may want
their arms longer to improve appearance and function.
Lengthening of the ulna can be performed using
an external fixator and gradual distraction. However,
this forearm lengthening is laborious and can require
extended periods of time in the device waiting for bony
consolidation (Figure 14).