Section 10 - Cystic Fibrosis Clinical Care Pathway

15 or 16. Young adults are usually transferred to an adult CF clinic in their
16th year. We normally refer to the Royal Brompton Hospital, the London
Chest Hospital and Papworth Hospital, although some children prefer to go
to centres closer to their home. Transition clinics are held at GOSH in the
out patient clinic with each of the above adult centres at least once a year.
These are a multidisciplinary team clinic with both adolescents and parents
invited. Informal visits can be arranged with the clinical nurse specialist at the
adult centre during these clinics.
The CF Clinic is held every Tuesday afternoon in Medical Outpatients (B)
from 2pm onwards for about 12 patients.
Every Clinic is attended by:
Two Consultants
Cystic Fibrosis Fellow
Physiotherapist and Physiotherapy Assistant
Lung Function Technician
Dietitian
Clinical Nurse Specialists (CNS)
Clinical Psychologist
Routine clinic procedure
• Height and weight are recorded by the clinic staff. If there has been any
weight loss urinalysis for glucose should be carried out.
• Physiotherapy assessment including review of technique and sputum or
throat swab is taken (please remember to sign and complete
microbiology request form).
• Spirometry and oxygen saturation (SaO2) are measured on all children
over five years of age and SaO2 alone in those under five.
• Dietary assessment and advice is available to all patients.
• The clinical nurse specialists are available to discuss various issues with all
children and families, including schooling, nebuliser equipment,
disability living allowances, etc.
• Patients’ notes are distributed between the consultants unless a specific
patient request is made. Patients attending for annual review follow up
should be seen by a consultant.
• The assessment by the medical staff pays particular attention to the
control of lung disease, the growth and development of the child, their
nutritional status and to early intervention to minimise complications.
• A clinical psychologist is available to see patients and their families in
clinic.
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