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Printable Test Catalog - OU Medicine

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[PORPHRAN] Urine Random Porphobilinogen<br />

SPECIMEN REQUIRED: Frozen urine (random)<br />

TUBE OR CONTAINER: Plastic urine container<br />

SPECIAL HANDLING: No preservative required unless ordered with<br />

Delta ALA, then specimen must be acidified<br />

with 0.5 mL 30% glacial acetic acid;<br />

Protect specimen from light:<br />

SPECIMEN VOLUME: 10 mL<br />

MINIMUM VOLUME: 1 mL<br />

TEST AVAILABILITY: Daily<br />

REFERENCE RANGE: 0.0-2.0 mg/L<br />

METHODOLOGY: Chromatography/spectrophotometry<br />

CLINICAL USE: Detect porphyrias and porphyrinurias<br />

CPT: 84110<br />

[PORPHTM] UR PORPHOBILINOGEN TIMED<br />

SPECIMEN REQUIRED: Frozen urine (24 hour)<br />

TUBE OR CONTAINER: Plastic urine container<br />

SPECIAL HANDLING: Collect in "A" container (30 mL of 33% glacial<br />

acetic acid); refrigerate specimen during<br />

collection; aliquot and FREEZE immediately;<br />

protect specimen from light<br />

SPECIMEN VOLUME: 10 mL<br />

MINIMUM VOLUME: 1 mL<br />

TEST AVAILABILITY: Daily<br />

REFERENCE RANGE: 0.0-1.5 mg/24 hours<br />

METHODOLOGY: Ion-exchange chromatography/spectrophotometry<br />

CLINICAL USE: Initial test for acute intermittent porphyria<br />

CPT: 84110<br />

[PORPHURAN] PORPHYRINS URINE RANDOM<br />

SPECIMEN REQUIRED: Refrigerated random urine<br />

TUBE OR CONTAINER: Plastic urine container<br />

SPECIAL HANDLING: Protect specimen from light<br />

SPECIMEN VOLUME: 2 mL<br />

MINIMUM VOLUME: 1.5 mL<br />

TEST INCLUDES: Coproporphyrins, uroporphyrins, heptacarboxlyporphyrins,<br />

pentacarboxylporphyrins,<br />

hexacarboxylporphyrins<br />

TEST AVAILABILITY: Daily<br />

TURNAR<strong>OU</strong>ND TIME: 2-5 days<br />

REFERENCE RANGE: Coproporphyrin I: 0-15 g/L<br />

Coproporphyrin III: 0-49 g/L<br />

Heptacarboxylporphyrins: 0-2 g/L<br />

Hexacarboxylporphyrins: 0-1 g/L<br />

Pentacarboxylporphyrins: 0-2 g/L<br />

Uroporphyrins: 0-20 g/L<br />

OTHER NAMES: Coproporphyrin; Uroporphyrin<br />

METHODOLOGY: High-pressure liquid chromatography (HPLC) with

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