DSM+II+1968

DEFINITIONS OF TERMS 19
by diffuse demyelination of the white matter with resulting diffuse
glial sclerosis and accompanied by intellectual deterioration. These
diseases are often familial in character and when possible should be
specified under the following:
Acute infantile diffuse sclerosis (Krabbe's disease).
Diffuse chronic infantile sclerosis (Merzbacher-Pelizaeus disease,
Aplasia axialis extracorticalis congenita).
Infantile metachromatic leukodystrophy (Greenfield's disease).
Juvenile metachromatic leukodystrophy (Scholz' disease).
Progressive subcortical encephalopathy (Encephalitis periaxialis
diffusa, Schilder's disease).
Spinal sclerosis (Friedreich's ataxia). Characterized by cerebellar
degeneration, early onset followed by dementia.
Encephalopathy, other, due to unknown or uncertain cause with the
structural reactions manifest. This category includes cases of mental
retardation associated with progressive neuronal degeneration or other
structural defects which cannot be classified in a more specific,
diagnostic category.
.4 Associated with diseases and conditions due to unknown prenatal
influence
This category is for classifying conditions known to have existed al
the time of or prior to birth but for which no definite etiology can be
established. These include the primary cranial anomalies and congenital
defects of undetermined origin as follows:
Anencephaly (including hemianencephaly).
Malformations of the gyri. This includes agyria, macrogyria (pachygyria)
and microgyria.
Porencephaly, congenital. Characterized by large funnel-shaped cavities
occurring anywhere in the cerebral hemispheres. Specify, il
possible, whether the porencephaly is a result of asphyxia at birtl
or postnatal trauma.
Multiple-congenital anomalies of the brain.
Other cerebral defects, congenital.
Craniostenosis. The most common conditions included in thi)
category are acrocephaly (oxycephaly) and scaphocephaly. Thes<
may or may not be associated with mental retardation.