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Colons epiteliale tumorer - Gastro.patologi.org

Colons epiteliale tumorer - Gastro.patologi.org

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Hereditær Non Polyposis Colorectal Cancer (HNPCC)<br />

• Klinik<br />

– Der opstår ikke flere adenomer, men hyppigere<br />

mutationer og dermed hurtigere progression<br />

– Ofte synkrone eller metakrone <strong>tumorer</strong><br />

– Ca. 80% af mutationsbærerne vil få KRC og/eller<br />

endometriecancer i en relativ ung alder<br />

– Cancer i nyrer, ovarier og ventrikel forekommer<br />

hyppigere hos disse patienter<br />

– Patienterne har generelt en bedre prognose end<br />

patienter med sporadisk KRC (MSS)

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