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Colons epiteliale tumorer - Gastro.patologi.org

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Familiær Adenomatøs Polypose (FAP)<br />

• Undertyper<br />

– FAP (≥100 kolorektale adenomer)<br />

– Gardner syndrom (+epidermoid cyster, osteomer, tandanomalier og<br />

desmoid <strong>tumorer</strong> (mesenteriel fibromatose))<br />

– Turcot syndrom (+hjerne<strong>tumorer</strong> – medulloblastom)<br />

– Attenuated FAP (

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